Multimodality Imaging in Restrictive Cardiomyopathies: An EACVI expert consensus document In collaboration with the "Working Group on myocardial and pericardial diseases" of the European Society of Cardiology Endorsed by The Indian Academy of Echocardiography
Volume
18
Pagination
1090 - +
Publisher
DOI
10.1093/ehjci/jex034
Journal
EUROPEAN HEART JOURNAL-CARDIOVASCULAR IMAGING
Issue
ISSN
2047-2404
Metadata
Show full item recordAbstract
Restrictive cardiomyopathies (RCMs) are a diverse group of myocardial diseases with a wide range of aetiologies including familial, genetic,
and acquired diseases and ranging from very rare to relatively frequent
cardiac disorders. This diversity is also reflected in the inconsistent classification of RCM across guidelines1–3 and even in the term ‘restrictive’,
which is a functional characterization, unlike the morphological definition of the three other main types of cardiomyopathies, i.e. hypertrophic, arrhythmogenic right ventricular or dilated cardiomyopathies.4
Independently of the underlying cause, the pathophysiology, and
clinical presentation, the initial phenotypic diagnosis of RCM requires
imaging techniques. Many advances have occurred in the last decade
in the diagnostic and prognostic assessment of RCM. This EACVI
consensus document provides comprehensive information for the
appropriateness of all non-invasive imaging techniques for the diagnosis, prognostic evaluation, and management of patients with RCM.
This article was written in close collaboration between the
European Association of Cardiovascular Imaging (EACVI) and the
Working Group (WG) on Myocardial and Pericardial diseases of
the European Society of Cardiology (ESC). The types of RCM covered in this document are those included in the classification system
proposed by the WG on Myocardial and Pericardial diseases1 as well
as some non-sarcomeric hypertrophic cardiomyopathies (HCMs)
with a restrictive physiology that in previous classifications were
included in the RCM category, e.g. cardiac amyloidosis (CA).
Authors
Habib, G; Bucciarelli-Ducci, C; Caforio, ALP; Cardim, N; Charron, P; Cosyns, B; Dehaene, A'L; Derumeaux, G; Donal, E; Dweck, MRCollections
- NIHR Advanced Imaging [366]